FB2025_05 , released December 11, 2025
FB2025_05 , released December 11, 2025
CV Term Report
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General Information
Term desquamative interstitial pneumonia ID (Ontology) DOID:0050158 (Human Disease)
Definition An idiopathic interstitial pneumonia that is characterized by the accumulation of bronchiolocentric alveolar macrophages in alveolar spaces and interstitial inflammation and involves mild bronchiolar fibrosis and chronic inflammation.
Also Known As "familial desquamative interstitial pneumonitis" ; "RBILD" ; "respiratory bronchiolitis-associated interstitial lung disease"
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Spanning Tree (Parents/Children)
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  pneumonia
   |__idiopathic interstitial pneumonia
       |__desquamative interstitial pneumonia
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Is a idiopathic interstitial pneumonia
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Synonyms
  • "familial desquamative interstitial pneumonitis" EXACT
    "RBILD" EXACT OMO:0003012
    "respiratory bronchiolitis-associated interstitial lung disease" EXACT
Secondary IDs
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ICD10CM:J84.117
ICD9CM:516.37
MESH:C562470
MIM:263000
NCI:C35288
SNOMEDCT_US_2023_03_01:8549006
UMLS_CUI:C0238378