FB2025_05 , released December 11, 2025
FB2025_05 , released December 11, 2025
CV Term Report
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General Information
Term arrhythmogenic left ventricular cardiomyopathy ID (Ontology) DOID:0070534 (Human Disease)
Definition An intrinsic cardiomyopathy characterized by hypokinetic, non-dilated, fibrotic or fibrofatty left ventricular myocardium and ventricular arrhythmias with a right bundle branch block pattern, with limited to no involvement of the right ventricle.
Also Known As "ALVC" ; "left ventricular ACM" ; "left-dominant arrhythmogenic cardiomyopathy"
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  cardiomyopathy
   |__intrinsic cardiomyopathy
       |__arrhythmogenic left ventricular cardiomyopathy
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Is a intrinsic cardiomyopathy
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Synonyms
  • "ALVC" EXACT OMO:0003012
    "left ventricular ACM" EXACT
    "left-dominant arrhythmogenic cardiomyopathy" EXACT
Secondary IDs
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ORDO:293888