FB2025_05 , released December 11, 2025
FB2025_05 , released December 11, 2025
CV Term Report
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General Information
Term blastic plasmacytoid dendritic cell neoplasm ID (Ontology) DOID:0081076 (Human Disease)
Definition An acute leukemia that is derived from the precursors of plasmacytoid dendritic cells, with a high frequency of cutaneous and bone marrow involvement and leukemic dissemination. Skin lesions appearing on the arms, legs, face and neck are the most common BPDCN symptom. Other symptoms include low counts of healthy blood cells and swollen lymph nodes.
Also Known As "Agranular CD4+ CD56+ Hematodermic Neoplasm/Tumor" ; "Agranular CD4+ Natural Killer Cell Leukemia" ; "Blastic Natural Killer Leukemia/Lymphoma" (for all, see Synonyms field below)
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  lymphoid leukemia
   |__acute leukemia
       |__blastic plasmacytoid dendritic cell neoplasm
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Synonyms
  • "Agranular CD4+ CD56+ Hematodermic Neoplasm/Tumor" EXACT
    "Agranular CD4+ Natural Killer Cell Leukemia" EXACT
    "Blastic Natural Killer Leukemia/Lymphoma" EXACT
    "Blastic NK-Cell Lymphoma" EXACT
    "CD4+/CD56+ Hematodermic Neoplasm" EXACT
    "natural killer (NK) cell leukemia/lymphoma" EXACT
Secondary IDs
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NCI:C7203