FB2025_05 , released December 11, 2025
FB2025_05 , released December 11, 2025
CV Term Report
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General Information
Term sarcoma ID (Ontology) DOID:1115 (Human Disease)
Definition A cell type cancer that has_material_basis_in abnormally proliferating cells derives from embryonic mesoderm.
Also Known As "connective and soft tissue neoplasm" ; "tumor of soft tissue and skeleton"
Comment
Links to External Ontologies
DO.org
Annotations
Records annotated with this term OR any of its CHILD TERMS
Records annotated with this exact term (annotations to child terms are NOT included)
Data Class Field Records
Human Disease Models (FBhh)  DOID       1
show Full annotation statements including this term (annotations to child terms are NOT included), and relevant FlyBase records
 Full annotation statements 
Relevant FlyBase reports
 Genes Human Disease Models
 sarcoma       1      1
Spanning Tree (Parents/Children)
Only view relationship:
  cancer
   |__cell type cancer
       |__sarcoma  42 rec.
           |__anus sarcoma
           |__bile duct sarcoma
           |__bladder sarcoma
           |__central nervous system sarcoma
           |   |__central nervous system angiosarcoma
           |   |__central nervous system fibrosarcoma
           |__central nervous system teratoma
           |   |__adult central nervous system teratoma(+)
           |   |__central nervous system immature teratoma(+)
           |   |__central nervous system mature teratoma(+)
           |__clear cell sarcoma
           |__colon sarcoma
           |   |__colon Kaposi sarcoma
           |__dendritic cell sarcoma
           |   |__follicular dendritic cell sarcoma
           |__epithelioid sarcoma
           |   |__adult epithelioid sarcoma
           |   |__central epithelioid sarcoma(+)
           |   |__childhood epithelioid sarcoma
           |   |__peripheral epithelioid sarcoma
           |__esophagus sarcoma
           |   |__esophagus leiomyosarcoma
           |__Ewing sarcoma 16 rec.
           |   |__Askin's tumor
           |   |__Ewing sarcoma of bone(+)
           |   |__extraosseous Ewing sarcoma(+)
           |__gallbladder sarcoma
           |__germ cell and embryonal cancer
           |   |__teratocarcinoma
           |   |__teratoma(+)
           |   |__trophoblastic neoplasm(+)
           |__Langerhans cell sarcoma
           |__larynx sarcoma
           |__leptomeninges sarcoma
           |__liposarcoma of the ovary
           |   |__myxoid liposarcoma of the ovary
           |__lung sarcoma
           |__malignant fibrous histiocytoma
           |   |__malignant inflammatory fibrous histiocytoma
           |__malignant hemangioma
           |   |__malignant epithelioid hemangioendothelioma
           |__mast-cell sarcoma
           |__mediastinum sarcoma
           |   |__mediastinal osteogenic sarcoma
           |__meninges sarcoma
           |   |__sarcomatosis of the meninges
           |__myxofibrosarcoma
           |__orbit sarcoma
           |   |__orbit rhabdomyosarcoma(+)
           |__ovarian angiosarcoma
           |__ovary sarcoma
           |   |__ovarian endometrioid stromal sarcoma
           |__pancreas sarcoma
           |__paranasal sinus sarcoma
           |__penis sarcoma
           |__prostate sarcoma
           |   |__prostate angiosarcoma
           |   |__prostate leiomyosarcoma
           |   |__prostate rhabdomyosarcoma(+)
           |   |__prostate stromal sarcoma
           |__rectum sarcoma
           |   |__rectum Kaposi's sarcoma
           |   |__rectum leiomyosarcoma
           |   |__rectum rhabdomyosarcoma
           |__rhabdomyosarcoma 24 rec.
           |   |__alveolar rhabdomyosarcoma 24 rec.
           |   |__anus rhabdomyosarcoma
           |   |__bile duct rhabdomyosarcoma(+)
           |   |__central nervous system rhabdomyosarcoma
           |   |__embryonal rhabdomyosarcoma(+)
           |   |__gallbladder rhabdomyosarcoma
           |   |__mediastinum rhabdomyosarcoma
           |   |__mixed type rhabdomyosarcoma
           |   |__oral rhabdomyosarcoma
           |   |__ovary rhabdomyosarcoma
           |   |__pleomorphic rhabdomyosarcoma(+)
           |   |__spindle cell rhabdomyosarcoma
           |__sarcomatosis
           |__skin sarcoma
           |   |__cutaneous leiomyosarcoma
           |   |__cutaneous liposarcoma
           |   |__skin angiosarcoma
           |__small cell sarcoma
           |   |__desmoplastic small round cell tumor
           |   |__EWSR1-negative small round cell tumor(+)
           |   |__round cell sarcoma with EWSR1-non-ETS fusion(+)
           |   |__sarcoma with BCOR genetic alterations(+)
           |__spinal cord sarcoma
           |__spindle cell sarcoma
           |__testis sarcoma
           |   |__testis rhabdomyosarcoma
           |__thyroid sarcoma
           |   |__thyroid angiosarcoma
           |__trachea sarcoma
           |__uterine corpus sarcoma
           |   |__uterine corpus endometrial stromal sarcoma
           |   |__uterus leiomyosarcoma(+)
           |__vagina sarcoma
           |   |__vagina leiomyosarcoma
           |   |__vaginal endometrial stromal sarcoma
           |__vulvar liposarcoma
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Is a cell type cancer
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Synonyms
  • "connective and soft tissue neoplasm" EXACT
    "tumor of soft tissue and skeleton" EXACT
Secondary IDs
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ICD10CM:C49
ICD9CM:171.9
ICDO:8800/3
SNOMEDCT_US_2023_03_01:93765001
UMLS_CUI:C0153519