FB2025_05 , released December 11, 2025
FB2025_05 , released December 11, 2025
CV Term Report
Help Close All Open All
General Information
Term connective tissue cancer ID (Ontology) DOID:201 (Human Disease)
Definition A musculoskeletal system cancer that is located_in connective tissue.
Also Known As "connective tissue neoplasm" ; "mesenchymal tissue malignant neoplasm" ; "neoplasm of connective tissues" (for all, see Synonyms field below)
Comment
Links to External Ontologies
DO.org
Annotations
Records annotated with this term OR any of its CHILD TERMS
Records annotated with this exact term (annotations to child terms are NOT included)
No relevant records available
show Full annotation statements including this term (annotations to child terms are NOT included), and relevant FlyBase records
 Full annotation statements 
Relevant FlyBase reports
 Genes
 for disease ribbon | Nezelof syndrome       1
 model of | Nezelof syndrome       1
Spanning Tree (Parents/Children)
Only view relationship:
organ system cancer
 |__musculoskeletal system cancer__
musculoskeletal system disease     |
 |__musculoskeletal system cancer__|
 |__connective tissue disease______|
                                   connective tissue cancer  24 rec.
                                    |__adult intracranial malignant hemangiopericytoma
                                    |__bone cancer 7 rec.
                                    |   |__adamantinoma(+)
                                    |   |__bone carcinoma(+)
                                    |   |__bone lymphoma
                                    |   |__bone sarcoma(+) 7 rec.
                                    |   |__chest wall bone cancer
                                    |   |__Ewing sarcoma of bone(+)
                                    |   |__femoral cancer
                                    |   |__jaw cancer(+)
                                    |   |__liposarcoma of bone
                                    |   |__long bones of lower limb cancer
                                    |   |__malignant neoplasm of short bones of lower limb
                                    |   |__notochordal cancer(+)
                                    |   |__orbital cancer(+)
                                    |   |__skull cancer(+)
                                    |   |__sternum cancer(+)
                                    |__cartilage cancer
                                    |__epithelioid sarcoma
                                    |   |__adult epithelioid sarcoma
                                    |   |__central epithelioid sarcoma(+)
                                    |   |__childhood epithelioid sarcoma
                                    |   |__peripheral epithelioid sarcoma
                                    |__Ewing sarcoma 16 rec.
                                    |   |__Askin's tumor
                                    |   |__Ewing sarcoma of bone(+)
                                    |   |__extraosseous Ewing sarcoma(+)
                                    |__fibrosarcoma
                                    |   |__adult fibrosarcoma
                                    |   |__central nervous system fibrosarcoma
                                    |   |__childhood fibrosarcoma(+)
                                    |   |__conventional fibrosarcoma
                                    |   |__dermatofibrosarcoma protuberans
                                    |   |__small bowel fibrosarcoma
                                    |__Kaposi's sarcoma
                                    |__lipofibromatosis-like neural tumor
                                    |__liposarcoma
                                    |   |__adult liposarcoma
                                    |   |__cellular myxoid liposarcoma
                                    |   |__childhood liposarcoma
                                    |   |__dedifferentiated liposarcoma
                                    |   |__esophagus liposarcoma
                                    |   |__fibroblastic liposarcoma
                                    |   |__intracranial liposarcoma
                                    |   |__kidney liposarcoma
                                    |   |__larynx liposarcoma
                                    |   |__liposarcoma of the ovary(+)
                                    |   |__mediastinum liposarcoma
                                    |   |__mixed liposarcoma
                                    |   |__myxoid liposarcoma(+)
                                    |   |__pleomorphic liposarcoma
                                    |   |__vulvar liposarcoma
                                    |   |__well-differentiated liposarcoma(+)
                                    |__malignant fibrous histiocytoma of bone
                                    |__malignant giant cell tumor
                                    |   |__bone giant cell sarcoma
                                    |   |__malignant giant cell tumor of soft parts
                                    |__mesenchymoma
                                    |   |__malignant mesenchymoma(+)
                                    |__myxosarcoma
                                    |__perivascular tumor
                                    |   |__hemangiopericytic tumor(+)
                                    |   |__pericytoma with t(7;12)
                                    |   |__perivascular epithelioid cell tumor(+)
                                    |__pleural cancer 2 rec.
                                    |   |__malignant parietal pleura tumor
                                    |   |__malignant pleural mesothelioma(+) 2 rec.
                                    |   |__malignant pleural solitary fibrous tumor
                                    |   |__malignant visceral pleura tumor
                                    |__solitary fibrous tumor/hemangiopericytoma
                                    |__synovium cancer
                                        |__malignant giant cell tumor of the tendon sheath
                                        |__synovial sarcoma(+)
Spanning Tree View Settings
Parents/Children
View Depth
Show hierarchy levels: for parents, for children
hide Relationships
Is a musculoskeletal system cancer
connective tissue disease
Part of
hide Synonyms & Secondary IDs
Synonyms
  • "connective tissue neoplasm" EXACT
    "mesenchymal tissue malignant neoplasm" EXACT
    "neoplasm of connective tissues" EXACT
    "Tumour of connective tissue" EXACT
Secondary IDs
hide External Crossreferences & Linkouts
MESH:D009372
SNOMEDCT_US_2023_03_01:126598008
UMLS_CUI:C0027656