FB2025_05 , released December 11, 2025
FB2025_05 , released December 11, 2025
CV Term Report
Help Close All Open All
General Information
Term lymphangioleiomyomatosis ID (Ontology) DOID:3319 (Human Disease)
Definition A lung disease that is characterized by progressive cystic destruction of the lung and lymphatic abnormalities, frequently associated with renal angiomyolipomas.
Also Known As "lung lymphangioleiomyomatosis" ; "lymphangiomyomatosis" ; "pulmonary lymphangioleiomyomatosis"
Comment
Links to External Ontologies
DO.org
Annotations
Records annotated with this term OR any of its CHILD TERMS
    Results list data from multiple species. Click on a button above and use the 'Filter by species' options on the resulting HitList to retrieve species-specific data.
Records annotated with this exact term (annotations to child terms are NOT included)
No relevant records available
show Full annotation statements including this term (annotations to child terms are NOT included), and relevant FlyBase records
 Full annotation statements 
Relevant FlyBase reports
 Genes
 lymphangioleiomyomatosis       2
 for disease ribbon | lymphangioleiomyomatosis       2
 model of | lymphangioleiomyomatosis       2
Spanning Tree (Parents/Children)
Only view relationship: 
  lower respiratory tract disease
   |__lung disease
       |__lymphangioleiomyomatosis  2 rec.
Spanning Tree View Settings
Parents/Children
View Depth
Show hierarchy levels: for parents, for children
hide Relationships
Is a lung disease
Part of
hide Synonyms & Secondary IDs
Synonyms
  • "lung lymphangioleiomyomatosis" EXACT
    "lymphangiomyomatosis" EXACT
    "pulmonary lymphangioleiomyomatosis" EXACT
Secondary IDs
hide External Crossreferences & Linkouts
GARD:3319
ICDO:9174/1
MIM:606690
NCI:C38153
ORDO:538
SNOMEDCT_US_2023_03_01:277844007
UMLS_CUI:C0349649