FB2025_05 , released December 11, 2025
FB2025_05 , released December 11, 2025
CV Term Report
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General Information
Term high grade ependymoma ID (Ontology) DOID:5074 (Human Disease)
Definition A high grade glioma that is derived from ependymal cells, a type of glial cell, located_in ventricle lining within the central part of the brain.
Also Known As "Ependymal neoplasm" ; "ependymal tumors" ; "malignant ependymoma"
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cell type cancer
 |__high grade glioma__________
cerebrum cancer                |
 |__cerebral ventricle cancer__|
                               high grade ependymoma
                                |__anaplastic ependymoma
                                |__brain stem ependymoma
                                |__childhood ependymoma
                                |__malignant adult ependymoma
                                |__posterior fossa ependymoma
                                |   |__posterior fossa group A ependymoma
                                |   |__posterior fossa group B ependymoma
                                |__spinal cord ependymoma
                                |   |__adult spinal cord ependymoma
                                |   |__spinal ependymoma, MYCN-amplified
                                |__supratentorial ependymoma
                                    |__RELA fusion-positive ependymoma
                                    |__supratentorial ependymoma, YAP1 fusion–positive
                                    |__supratentorial ependymoma, ZFTA fusion–positive
                                    |__YAP1-MAMLD1 fusion-positive supratentorial ependymoma
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Is a high grade glioma
cerebral ventricle cancer
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Synonyms
  • "Ependymal neoplasm" EXACT
    "ependymal tumors" EXACT
    "malignant ependymoma" EXACT
Secondary IDs
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ICDO:9391/3
NCI:C6770
UMLS_CUI:C1333407