FB2025_05 , released December 11, 2025
FB2025_05 , released December 11, 2025
CV Term Report
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General Information
Term primary pulmonary hypertension ID (Ontology) DOID:14557 (Human Disease)
Definition A chronic pulmonary heart disease characterized by an increase of blood pressure in the pulmonary artery, pulmonary vein, or pulmonary capillaries, among others, has symptoms shortness of breath, dizziness, fainting, leg swelling.
Also Known As "Idiopathic pulmonary arterial hypertension"
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 Genes
 primary pulmonary hypertension       5
 for disease ribbon | primary pulmonary hypertension       5
 model of | primary pulmonary hypertension       5
Spanning Tree (Parents/Children)
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polygenic disease
 |__digenic disease__________________
Cor pulmonale                        |
 |__chronic pulmonary heart disease__|
                                     primary pulmonary hypertension  5 rec.
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chronic pulmonary heart disease
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Synonyms
  • "Idiopathic pulmonary arterial hypertension" EXACT
Secondary IDs
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ICD10CM:I27.0
ICD9CM:416.0
MIM:178600
MIM:265400
MIM:615342
MIM:615343
MIM:615344
ORDO:422
SNOMEDCT_US_2023_03_01:26174007
UMLS_CUI:C0152171