FB2025_05 , released December 11, 2025
FB2025_05 , released December 11, 2025
CV Term Report
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General Information
Term scimitar syndrome ID (Ontology) DOID:4297 (Human Disease)
Definition A congenital heart disease that is characterized by partial or entire anomalous curved venous drainage of the right lung to the inferior vena cava, association with variable right lung and pulmonary artery hypoplasia, dextraposition of the heart and an anomalous systemic blood supply to the ipsilateral lung.
Also Known As "congenital venolobar syndrome" ; "Halasz syndrome" ; "hypogenetic lung syndrome" (for all, see Synonyms field below)
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Spanning Tree (Parents/Children)
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physical disorder__
heart disease______|
                   congenital heart disease
                    |__scimitar syndrome
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Is a congenital heart disease
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Synonyms
  • "congenital venolobar syndrome" EXACT
    "Halasz syndrome" EXACT
    "hypogenetic lung syndrome" EXACT
    "mirror-image lung syndrome" EXACT
    "pulmonary venolobar syndrome" EXACT
    "total anomalous pulmonary venous return" EXACT
    "vena cava bronchovascular syndrome" EXACT
Secondary IDs
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ICD10CM:Q26.8
MESH:D012587
MIM:106700
NCI:C85056
ORDO:185
SNOMEDCT_US_2023_03_01:39905002
UMLS_CUI:C0036400