FB2025_05 , released December 11, 2025
FB2025_05 , released December 11, 2025
CV Term Report
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General Information
Term cholangiocarcinoma ID (Ontology) DOID:4947 (Human Disease)
Definition A bile duct adenocarcinoma that has_material_basis_in bile duct epithelial cells.
Also Known As "adult primary Cholangiocarcinoma" ; "adult primary cholangiocellular carcinoma" ; "cholangiosarcoma"
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adenocarcinoma_______
bile duct carcinoma__|
                     bile duct adenocarcinoma
                      |__cholangiocarcinoma
                          |__extrahepatic bile duct carcinoma
                          |   |__extrahepatic bile duct adenocarcinoma(+)
                          |   |__extrahepatic bile duct leiomyosarcoma
                          |__intrahepatic cholangiocarcinoma
                              |__cholangiolocellular carcinoma
                              |__Klatskin's tumor
                              |__mucinous intrahepatic cholangiocarcinoma
                              |__sarcomatous intrahepatic cholangiocarcinoma
                              |__signet ring cell intrahepatic cholangiocarcinoma
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Is a bile duct adenocarcinoma
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Synonyms
  • "adult primary Cholangiocarcinoma" EXACT
    "adult primary cholangiocellular carcinoma" EXACT
    "cholangiosarcoma" EXACT
Secondary IDs
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ICD10CM:C22.1
ICDO:8160/3
MESH:D018281
NCI:C4436
NCI:C8265
SNOMEDCT_US_2023_03_01:70179006
UMLS_CUI:C0206698
UMLS_CUI:C0280725